Michael
 
John
 
Bennett
PhD
Email: 
bennettmi@email.chop.edu
Address: 
5NW58 CHOP Main Building
215-590-3394
Affiliations
Expertise

Pediatric Clinical Chemistry with an emphasis on inborn errors of metabolism. Director of a full service metabolic disease laboratory.

1. Define genetic defects of mitochondrial fatty acid oxidation, identify diagnostic biomarkers and study intramitochondrial compartmentalization of matrix proteins
2. Study basic elements of neuronal death in neuronal ceroid-lipofuscinosis ( Batten disease) and develop an animal model to test therapies to prevent neuronal death

Disorders of mitochondrial fatty acid oxidation with an emphasis on control of insulin secretion by short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency. The Neuronal-Ceroid Lipofuscinoses. A stufdy of the function of CLN3P, the protein responsible for Juvenile Batten Disease

Appointments
Professor of Pathology and Laboratory Medicine at the Children's Hospital of Philadelphia (2004– present)
Education
PhD, Clinical Enzymology, University of Sheffield School of Medicine (1976)
BSc, Physiology & Biochemistry, Reading University, UK (1972)
Selected Publications